Managing the diet

A summery of PKU Formulas.

Here is a summery of as many formulas I can think of. ( wording is not my own, information taken from the websites provided) Please be sure to check with your dietitians and medical staff before requesting a sample or switching formula.

Applied Nutrition: 

http://www.medicalfood.com 

Phenyl Ade Essentials : 

The only PKU formula with flax & soluble fiber to support heart health

American Heart Association recommend 4:1 ratio of Omega-6 to Omega-3

Complete with essential vitamins and minerals to help meet daily requirements

5 great choices: Chocolate, Vanilla, Orange Creme, Strawberry and Unflavored

Packaged in cans and convenient ‘go anywhere’ single serve pouches

Suitable for individuals over 1 year of age with proven PKU

PhenylAde Essential Drink Mix is the foundation for building a healthy PKU diet. This great tasting PKU product provides an ideal blend of vitamins and minerals with a superior amino acid profile to meet the needs of children, teens and adults following a PKU diet. PhenylAde Essential contains less saturated fat than other leading PKU formulas with added fiber and flax to support heart health

Phenyl ade RTD 10 :

  • Only 60 calories per bottle
  • Complete with essential vitamins and minerals
  • 10g protein equivalents in each 2.5 fl oz bottle
  • No preservatives
  • No artificial colors or flavors
  • Suitable for individuals over 4 year of age with proven PKU

PhenylAde RTD is a ready to drink PKU formula. This great tasting PKU product helps you meet your full daily prescription in less total volume by supplying 10 grams of protein equivalent in each 2.5 fluid ounce bottle. PhenylAde RTD is complete with vitamins and minerals including a superior amino acid profile to meet the needs of children, teens and adults following a PKU diet.

Phenyl Ade 40: 

  • Only 1/2 gram of fat per serving
  • Reduced volume for easier dietary compliance
  • Complete with essential vitamins and minerals to help meet daily requirements
  • Available in convenient ‘go anywhere’ single-serve pouches
  • Mild, neutral flavors allows for easy drinking
  • Suitable for individuals over 1 year of age with proven PKU

PhenylAde40 Drink Mix is a reduced calorie, fat and volume PKU formula. This great tasting PKU product helps you meet your full daily prescription in less total volume. It provides an ideal blend of vitamins and minerals with a superior amino acid profile to meet the needs of children, teens and adults following a PKU diet.

 

Phenyl Ade 60 :

  • Only 50 calories per serving
  • Excellent for weight management
  • Low volume for easier dietary compliance
  • Complete with essential vitamins and minerals to help meet daily requirements
  • Available in cans and convenient ‘slimline’ single-serve pouches
  • Suitable for individuals over 1 year of age with proven PKU

PhenylAde60 Drink Mix is a high protein, low calorie, low volume PKU formula. This great tasting PKU product mixes easily with only 3 fluid ounces of cold water allowing you to meet your full daily prescription with less to drink. The superior amino acid profile and full range of vitamins and minerals help meet the needs of older children, teens and adults following a PKU diet.

Phenyl ade Amino Acid Blends::

  • Create your own PKU formula by adding to low protein foods or drinks
  • Fat free, sugar free & low calorie
  • Tasteless and Odorless
  • Boost amino acid protein intake by adding to current PKU formula
  • Available in cans and convenient ‘slimline’ single serve pouches
  • Suitable for individuals over 1 year of age with proven PKU

PhenylAde Amino Acid Blend and MTE Amino Acid Blend are a precise mixture of essential and nonessential amino acids for the dietary management of Phenylketonuria (PKU). These products allow you to “create your own PKU formula” to improve taste, variety and flexibility to reduce formula fatigue and improve diet compliance.

 

Phenyl Ade Amino Acid Bars: 

  • An alternative to liquid PKU formula
  • Packaged in convenient “go anywhere” travel bars
  • Available in a great tasting Chocolate, Chocolate Crispy and White Chocolate flavors
  • Suitable for individuals over 1 year of age with proven PKU

PhenylAde Amino Acid Bars are an innovative medical food intended to provide an alternative source of protein, fat and carbohydrate for the dietary management of PKU. PhenylAde Amino Acid Bars can supplement all or part of the protein prescription when traditional liquid formula is insufficient or not tolerated. Available in 3 delicious flavors, PhenylAde Amino Acid Bars look, taste and smell like real chocolate.

 

Phenyl Ade PheBlock : 

  • Simplifies PKU diet management
  • An alternative to PKU drug therapy
  • Allows for a relaxed PKU diet
  • Eliminates need for expensive low protein foods
  • Available in Tablets or Powder
  • Suitable for individuals over 12 years of age with proven PKU

PheBLOC LNAA allows for a relaxed PKU diet which includes more choices of natural protein from a wide variety of foods. The relaxed PheBLOC LNAA diet helps to reduce the burden of high priced, low protein specialty products. You will have more choices in restaurants and social settings making the diet less complicated.

SHS Nutricia 

http://nutrition.nutricia.com/ as well as  https://www.myspecialdiet.com/ and http://www.nutricia-na.com/index.htm

Add-ins:

Add-ins is a flavourless phenylalanine-free powder containing balanced amounts of the other essential and non-essential amino acids, fat, vitamins, trace elements, calcium, phosphorus and magnesium.

Easiphen:( 8 years and up) 

Easiphen is a ‘ready to drink’ phenylalanine free liquid product containing a balanced mixture of essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements. Available in Forest Berries flavour. A food for special medical purposes.

Liquid Duocal : 

Liquid Duocal is an emulsion consisting of a blend of carbohydrate and fat. A food for special medical purposes.

Lophelx LQ 10 : ( 4 years and up) 

A flavoured phenylalanine-free liquid containing a balanced mixture of the other essential and non-essential amino acids, vitamins, trace elements and some minerals. A food for special medical purposes. Comes in Berry, Juicy Orange, and Tropical

Minaphelx: ( ages 1 to 10 ) 

Minaphlex is a palatable phenylalanine free drink mix containing essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements. Available in Unflavoured, Pineapple & Vanilla or Chocolate flavour (contains colour, sugar and sweeteners). A food for special medical purposes.

 

Phelxy 10 bars : ( 8 years and up) 

The Phlexy-10 Bars is a citrus fruit flavoured bar free from phenylalanine, but containing a balanced mixture of essential and non-essential amino acids, fat, carbohydrate and colouring. A food for special medical purposes.

Phlexy 10 Capsules: ( 8 years and up) 

Phlexy-10 Capsules are cellulose capsules, free from phenylalanine but containing a balanced mixture of essential and non-essential amino acids. A food for special medical purposes.

Phlexy 10 – Drink Mix ( 8 years and up) 

Phlexy-10 Drink Mix is a flavoured powder, free from phenylalanine but containing a balanced mixture of essential and non-essential amino acids, carbohydrate, colouring, sweetener and flavouring. Available in Citrus Burst, Apple and Blackcurrant and Tropical Surprise Flavours. A food for special medical purposes.

Phlexy 10 – tablets ( 11 years and up )  

PHLEXY-10 Tablets are free from phenylalanine but containing a balanced mixture of essential and non-essential amino acids. A food for special medical purposes.

Phlexy Vits: (ages 11 and up )

Phlexy-Vits is a concentrated powdered vitamin, mineral and trace element preparation. A food for special medical purposes.

Phlexy Vits Tablets : ( 11 years and up ) 

Phlexy-Vits are tablets containing vitamins, minerals and trace elements.

PK-Aid 4 ( 6 months and up) 

PK Aid-4 is a phenylalanine free unflavoured blend of essential and non-essential amino acids. A food for special medical purposes.

Anamix  Junior LQ : (1 to 10 years ) 

A phenylalanine-free drink containing a balanced mix of the other essential and non-essential amino acids, carbohydrates, fat (including docosahexanoic acid (DHA)), vitamins, minerals and trace elements. Available as unflavoured, orange or berry flavoured.

Lophlex LQ 20 ( 4 years and up) 

Lophlex LQ is a “ready to drink,” phenylalanine-free liquid containing a balanced mixture of essential and non-essential amino acids, carbohydrates, vitamins, trace elements and some minerals. Available in Berry, Orange and Citrus flavours. A food for special medical purposes.

XP Analog :( 0 to 1 years ) 

XP Analog is a phenylalanine free powdered infant feed, containing essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals, and trace elements. A food for special medical purposes.

XP Analog LCP ( 0 to 1 year) 

XP Analog LCP is a phenylalanine free powdered infant feed supplemented with long chain polyunsaturated fatty acids (LCPUFA’s), particularly Docosahexaenoic Acid (DHA) and Arachidonic Acid (AA), containing essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals, and trace elements. A food for special medical purposes.

XP Maxamaid : ( 1 to 8 years)

XP Maxamaid is a phenylalanine free drink mix containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. Available in Orange flavour (contains colours, sugar and sweeteners) or Unflavoured. A food for special medical purposes.

XP Maxamum : ( 8 years and over) ( powder) 

XP Maxamum is a phenylalanine free drink mix containing essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements. Available in Orange flavour (contains colours, sugar and sweeteners), Strawberry flavour (contains colours, sugar and sweeteners) or Unflavoured. A food for special medical purposes.

XP Maxamum Liquid TETRA Packs : ( 5 years and over) 

A flavored phenylalanine-free amino acid-based drink containing a balanced mix of the other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements for the dietary management of phenylketonuria (PKU). Suitable for ages 5 through adult, including pregnant women. Come in Forest Berry and Orange.

Periflex Infant

phenylalanine-free powdered infant formula with iron, containing DHA and ARA, for the dietary management of phenylketonuria (PKU).

 

 Periflex Junior

  • Phenylalanine-free
  • Easy transition from Periflex Infant
  • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, fat, vitamins, minerals and trace elements
  • Excellent balance of linoleic acid and α-linolenic acid, providing a preferable 4:1 ratio of n-6 to n-3
  • Age-appropriate DRI formulation
  • Periflex Junior provides 25 g of protein equivalent and 14 g of fat per 100 g of powder
  • Meets protein requirements in lower volume
  • Pleasant taste, smell and texture
  • Available in unflavored and orange
  • Optimal nutrition of all ages
  • Osmolality (mOsm/kg)

Preiflex Advance : 

A phenylalanine-free, powdered medical food for the dietary management of phenylketonuria (PKU) in older children and adults, including pregnant women and women of child-bearing age.

Milupa PKU 2: 

A phenylalanine-free powdered medical food for the dietary management of phenylketonuria (PKU) in children over 1 years of age.

Milupa PKU 3: 

A phenylalanine-free powdered medical food for the dietary management of phenylketonuria (PKU) for adolescents, adults, and pregnant women

Lanaflex : 

amino acids (large neutral amino acids and lysine) for the dietary management of phenylketonuria (PKU) in adults (over 18 years of age) who are no longer following a phenylalanine-restricted diet.

 

Vitaflo

http://www.vitafloweb.com/

PKU Start : ( birth to 1 years ) 

PKU start is a ready-to-feed phenylalanine free infant formula, containing essential and non essential amino acids, carbohydrate, fat, vitamins, minerals, trace elements and long chain polyunsaturated fatty acids (LCPs); Arachidonic acid (AA) and Docosahexaenoic acid (DHA)

PKU Squeezie ( 6 months to 10 years) 

PKU squeezie is an apple & banana flavoured ready-to-feed phenylalanine free protein substitute containing essential and non essential amino acids, carbohydrate, sugar, vitamins, minerals, trace elements and the long chain polyunsaturated fatty acids (LCPs); Arachidonic acid (AA) and Docosahexaenoic acid (DHA).

PKU Gel – ( 6 months to 10 years)

PKU gel is a powdered phenylalanine free protein substitute, available in unflavoured, orange and raspberry flavoured options, containing essential and non essential amino acids, carbohydrate, sugar, vitamins, minerals and trace elements. Flavoured options contain sweeteners.

PKU Cooler System: ( 3 years to adult) 

The PKU cooler® system is a range of ready-to-drink phenylalanine free protein substitutes, available in neutral-tasting (white), and flavoured (orange, purple and red) options, containing essential and non essential amino acids, carbohydrate, vitamins, minerals, trace elements and the Omega-3 long chain polyunsaturated fatty acids (LCPs); Docosahexaenoic acid (DHA) and Eicosapentaenoic acid (EPA). Contains sugar and sweeteners.

PKU Express System: ( 3 years to adult) 

PKU express is a range of powdered phenylalanine free protein substitute, available in unflavoured, orange, lemon and tropical flavoured options, containing essential and non essential amino acids, carbohydrate, sugar, vitamins, minerals and trace elements. Flavoured options contain sweeteners.

Cambrooke Foods

http://www.cambrookefoods.com/

Camino Pro Amino Acid : 

  • For PKU and MSUD patients age 5 and older
  • Ready-to-drink pouches
  • Available in Fruit Punch and Pina Colada flavors
  • Great flavor and no aftertaste
  • Reduced sugar and low volume
  • Complete with macronutrients, vitamins, minerals, and trace elements.

 

Bettermilk : 

A mix-with-liquid powdered formula for PKU that makes a creamy, milk-like beverage with a hint of sweetness.

BetterMilk™ 3-12 is designed with 10 grams of Glytactin and optimal age specific vitamins and minerals for those ages 3-12. It is available in two delicious flavors: orange creme and strawberry creme.

BetterMilk™ 12+ is designed with 15 grams of Glytactin and optimal age specific vitamins and minerals for those ages 12 and older. It is available in two delicious flavors: orange creme and strawberry creme.

BetterMilk™ original is designed with 15 grams of Glytactin and vitamins and minerals for those ages 1 and older. It is available in unflavored.

  • Made with Glytactin™ protein, our advanced proprietary blend of glycomacropeptide and essential amino acids, that is better utilized by your body.
  • Helps to better maintain blood Phe levels between meals.
  • Low volume – mix with 4 fluid ounces of water.
  • 32 mg of DHA Omega-3 Fatty Acids per serving (DHA Omega-3 for a healthy brain and heart!)
  • Probiotic cultures to support digestive health.
  • Great non-medicinal taste.
  • Combines well with your favorite foods.

Camino Pro Complete Bars: 

A complete and balanced meal for the PKU patient. It has age specific vitamins and minerals. Each bar includes, 15 grams of Glytacin, Vitamins, minerals, fiber, fat and carbohydrates. Comes in peanut butter and Fruit Frenzy flavors. Ready to eat. Each bar has 3 grams of fiber.

Restore: 

Restore has 10 grams of hole protein per 16.9 oz ( 500 ml) , is made with Glytacin. It includes amino acids, carbohydrates, electrolytes , B vitamins and is a source of calcium.  Restore is an isotonic beverage, that re-hydrates while you exercise and replaces electrolytes lost through perspiration. Comes in 2 flavors. Lemon Lime and Tangerine.

Camino Pro Swirl :

Camino Pro Swirl is the newest formula available.  It is a powdered formula that can be mixed with 3 to 4 ounces of cold water ( thick) to make a creamy pudding , or mix with 6- 8 ounces to make a shake or smoothie!

Swirl is made with 15 grams of Glytacin Protein. It is fortified with vitamins and minerals. Swirl is naturally high in the Large Neautral Amino Acids (LNAA’s) Threonine, isoleucine, and Valine. Each serving contains 32 mg of DHA Omega 3’s. Can be used as a meal replacement or a snack.

 

To the best of my knowledge, this may not be a complete list of all available formulas. If you know of any others please feel free to message me with information. As you can see, there is a such a variety. We are so blessed with the advancements of PKU through out the years in PKU formulas. I am forever grateful to all the low protein food companies and manufacturers of our formulas.   It is really incredible and inspiring to see such a variety today. Not all products are suitable for everyone with PKU and no 2 products are the same. If you wish to try any of these formulas please check out the websites listed for more information and consult your PKU clinic before requesting a sample.

 

 

 

 


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